Understanding TreatmentOptions in
Cutaneous Lymphoma
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5
Cutaneous T-Cell Lymphomas
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SECTION2:
CUTANEOUS T-CELL LYMPHOMAS
Cutaneous T-Cell Lymphoma Subtypes
CutaneousT-cell lymphomas (CTCLs) account for 75%–80% of all cutaneous
lymphomas.Mycosis fungoides is slow growing and is themost common
type, accounting for about 44% of all CTCLs.
1
Primary cutaneousCD30+
lymphoproliferative disorders are the secondmost common group ofCTCLs,
accounting for about 20% of all cases; they can be slow growing (lymphomatoid
papulosis) or fast growing (primary cutaneous anaplastic large-cell lymphoma).
Sézary syndrome is themost common fast-growingCTCL and accounts for
about 3% of all CTCLs.
Table1
shows the different types ofCTCLs.
Table1.
Types ofCTCLs
Additional information about the subtypes ofCTCL can be found at
.
Cutaneous T-Cell Lymphomas
(75%–80%of cutaneous lymphomas)
Mycosis fungoides
Sézary syndrome
Primary cutaneousCD30+ lymphoproliferative disorders
Lymphomatoidpapulosis
Primary cutaneous anaplastic large-cell lymphoma
Subcutaneous panniculitis-likeT-cell (
αβ
) lymphoma
Primary cutaneous extranodal natural killer/T-cell lymphoma, nasal
type
Primary cutaneous peripheralT-cell lymphoma
Primary cutaneousCD4+ small/mediumpleomorphicT-cell
lymphoma
Primary cutaneous aggressiveCD8+T-cell lymphoma
Cutaneous
γ
/
δ
T-cell lymphoma
